PAH type | Scotland [13] | USA [12] | France [17] | Spain [19] | USA/REVEAL [18] |
---|---|---|---|---|---|
n | 374 | 578 | 674 | 866 | 2525 |
Overall | 2.3:1 | 3.3:1 | 1.9:1 | 2.5:1 | 3.6:1 |
Idiopathic | 1.7:1 | 3:1 (with familial) | 1.6:1 | 2.7:1 | 4.1:1 |
Heritable | Â | 3:1 (with idiopathic) | 2.3:1 | Â | Â |
Congenital | 2.1:1 | 2.1:1 | 2:1 | 2.7:1 | Â |
Anorexigen-associated | Â | All female | 14.9:1 | Â | Â |
CTD-associated | 4.8:1 | 6.7:1 | 3.9:1 | 8.8:1 | 9:1 |
HIV-associated | Â | 1:7.7 | 1:1.2 | 1.5:1 | Â |
Portopulmonary hypertension | Â | 2.3:1 | 1:1.5 | 1:1 | Â |
Toxic oil syndrome | Â | Â | Â | 2.3:1 | Â |
Veno-occlusive disease | Â | Â | Â | 4:1 | Â |